Search on: NEVUS PHAKOMATOSIS, JADASSOHN 
Descriptors Found: 1
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Descriptor English:   Nevus, Sebaceous of Jadassohn 
Descriptor Spanish:   Nevo Sebáceo de Jadassohn 
Descriptor Portuguese:   Nevo Sebáceo de Jadassohn 
Synonyms English:   Epidermal Nevus, Verrucous
Feuerstein Mims Syndrome
Feuerstein-Mims Syndrome
Inflammatory Linear Verrucose Epidermal Nevus
Inflammatory Linear Verrucous Epidermal Naevus
Jadassohn Nevus Phakomatosis
Jadassohn Nevus Sebaceus
Jadassohn Sebaceous Nevus
Linear Sebaceous Nevus
Linear Sebaceous Nevus Syndrome
Linear Verrucous Epidermal Nevus
Nevus Phakomatoses, Organoid
Nevus Phakomatosis, Jadassohn
Nevus Phakomatosis, Organoid
Nevus Sebaceus of Jadassohn
Nevus, Linear Sebaceous
Nevus, Verrucous
Nevus, Verrucous Epidermal
Organoid Nevus Phakomatoses
Organoid Nevus Phakomatosis
Phakomatoses, Organoid Nevus
Phakomatosis, Jadassohn Nevus
Phakomatosis, Organoid Nevus
Schimmelpenning Feuerstein Mims Syndrome
Schimmelpenning Syndrome
Schimmelpenning-Feuerstein-Mims Syndrome
Sebaceous Nevus Syndrome, Linear
Sebaceous Nevus of Jadassohn
Sebaceous Nevus, Linear
Syndrome, Feuerstein-Mims
Syndrome, Schimmelpenning
Syndrome, Schimmelpenning-Feuerstein-Mims
Verrucous Epidermal Nevus
Verrucous Nevus  
Tree Number:   C04.557.665.560.700
C10.562.700
C16.131.077.633
Definition English:   A syndrome characterized by lesions occurring on the face, scalp, or neck which consist of congenital hypoplastic malformations of cutaneous structures and which over time undergo verrucous hyperplasia. Additionally it is associated with neurological symptoms and skeletal, ophthalmological, urogenital, and cardiovascular abnormalities. 
History Note English:   2010 (2008) 
Allowable Qualifiers English:  
BL blood CF cerebrospinal fluid
CI chemically induced CL classification
CO complications CN congenital
DI diagnosis DG diagnostic imaging
DH diet therapy DT drug therapy
EC economics EM embryology
EN enzymology EP epidemiology
EH ethnology ET etiology
GE genetics HI history
IM immunology ME metabolism
MI microbiology MO mortality
NU nursing PS parasitology
PA pathology PP physiopathology
PC prevention & control PX psychology
RT radiotherapy RH rehabilitation
SU surgery TH therapy
UR urine VE veterinary
VI virology  
Record Number:   52582 
Unique Identifier:   D054000 

Occurrence in VHL:
 

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